OAU - Overview: Organic Acids Screen, Urine

Test Catalog

Test Name

Test ID: OAU    
Organic Acids Screen, Urine

Useful For Suggests clinical disorders or settings where the test may be helpful

Diagnosis of inborn errors of metabolism


The urine organic acids (OAU) test provides a qualitative report of abnormal levels of organic acids identified via gas chromatography-mass spectrometry.


Diagnostic specificity of inborn errors of metabolism via urine organic acids is variable due to factors such as specimen collection when patient is asymptomatic versus acutely ill, taking dietary supplements, or anabolic versus catabolic.

Testing Algorithm Delineates situation(s) when tests are added to the initial order. This includes reflex and additional tests.

The following algorithms are available in Special Instructions:

-Newborn Screening Follow-up for Elevations of C8, C6, and C10 Acylcarnitines (also applies to any plasma or serum C8, C6, and C10 acylcarnitine elevations)

-Newborn Screening Follow-up for Isolated C4 Acylcarnitine Elevations (also applies to any plasma or serum C4 acylcarnitine elevation)

-Newborn Screening Follow-up for Isolated C5 Acylcarnitine Elevations (also applies to any plasma or serum C5 acylcarnitine elevation)

-Porphyria (Acute) Testing Algorithm

Special Instructions and Forms Describes specimen collection and preparation information, test algorithms, and other information pertinent to test. Also includes pertinent information and consent forms to be used when requesting a particular test

Method Name A short description of the method used to perform the test

Gas Chromatography-Mass Spectrometry (GC-MS)

NY State Approved Indicates the status of NY State approval and if the test is orderable for NY State clients.


Reporting Name A shorter/abbreviated version of the Published Name for a test; an abbreviated test name

Organic Acids Scrn, U

Aliases Lists additional common names for a test, as an aid in searching

2-Ketoadipic Acid
2-Ketoglutaric Acid
3-OH Dodecanedioic Acid
3-OH Sebacic Acid
4-OH Butyric Acid
Adipic Acid
Biotinidase Deficiency
Canavan Disease
Ethylmalonic Acid (EMA)
Fumaric Acid
Gamma-Hydroxybutyric (GHB) Acid
GHB (Gamma-Hydroxybutryic) Acid
Glutaric Acid
Glycerate, Urine, Qualitative
Homogentisic Acid
Lactic Acid
MADD (Multiple Acyl-CoA Dehydrogenase Deficiency)
Malonic Acid
Methylmalonic Acid (MMA)
Mevalonic Acid
MMA (Methylmalonic Acid)
Multiple Acyl-CoA Dehydrogenase Deficiency (MADD)
Multiple Carboxylase Deficiency
N-Acetyl Aspartic Acid
Nonvolatile and Volatile Organic Acids Screen
Octenedioic Acid
Propionic Acid
Pyroglutamic Acid
Pyruvic Acid
Sebacic Acid
Suberic Acid
Volatile and Nonvolatile Organic Acids Screen
Isovaleric Acid (IVA)