Unit Code 80619:
Organic Acids Screen, Urine
Useful For
Diagnosis of inborn errors of metabolism
Method Name
Gas Chromatography-Mass Spectrometry (GC-MS)
Reporting Name
Organic Acids Scrn, U
Ordering Mnemonic
OAU
Aliases
2-Ketoadipic Acid
2-Ketoglutaric Acid
3-OH Dodecanedioic Acid
3-OH Sebacic Acid
4-OH Butyric Acid
Adipic Acid
Alkaptonuria
Biotinidase Deficiency
Canavan Disease
EMA
Ethylmalonic Acid
Fumaric Acid
GA2
Gamma Hydroxybutyric Acid
Gamma OH-butyrate
GHB
Glutaric Acid
Glycerate, Urine, Qualitative
Isovaleric Acid
Lactic Acid
MADD
Malonic Acid
Methylmalonic Acid
Mevalonic Acid
MMA
Multiple Carboxylase Deficiency
N-Acetyl Aspartic Acid
Nonvolatile-Volatile
Octenedioic Acid
Proprionic Acid
Pyroglutamic Acid
Pyruvic Acid
Sebacic Acid
Suberic Acid
Succinylacetone
Volatile-Nonvolatile


